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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
60 %
Mots clés
Adipose tissue
Sarcopenia
Neuromuscular disease
2-D PAGE
ALS
Muscle fibrosis
Cross-bridge kinetics
Muscular dystrophy
Myosin
Mass spectrometry
Dysferlin
Fibrosis
Satellite cells
Epigenetics
BINDING SPECIFICITY
Effector T cells
Andermann syndrome
Agrégats de PABPN1
Neuromuscular junction NMJ
Alphavirus
Antisens oligonucleotides
GENE
APOPTOSIS
Inflammation
DUX4
Differentiation
PABPN1 agregates
AUTOPHAGY
Muscle dystrophy
MUTATIONS
Atrophy
Regulatory T cells
Anti-acetylcholine receptor antibodies
Oculopharyngeal muscular dystrophy
Biomarker
Intercellular communication
Myoblasts
Amyotrophic Lateral Sclerosis
Geriatric assessment
Autologous
Omics
Nuclear envelope
Metabolism
Thérapie génique
Arbovirus
Myogenesis
AChR antibodies
Haploinsufficiency
Gene replacement
Lamins
OPMD
Accelerometry
AAV
AAV vectors
Regenerative medicine
Dystrophie musculaire oculopharyngée
Duchenne muscular dystrophy
Dystrophin
Myoblast
Annexin A2
Human
Aggregate
PABPN1
DMD
Muscle
ARN
Exon-skipping
Myositis
Ageing
Alzheimer's disease
FSHD
Dysferlinopathy
FAPs
DNA methylation
Antiserum
Actin
Aav-U7
Triplet expansion disease
Gene therapy
Aged
Pax7
Calcium
Muscle stem cells
Anti-fibrotic pharmacotherapies
Autoimmune diseases
Satellite cell
Functional genomics
Myopathy
Regeneration
Myotube
Skeletal muscle
Muscle strength
Akt
Cell therapy
Transcriptomics
RNA
Bile salt hydrolases
Myopathies
Pharyngeal muscle
Xenograft